From: An investigation of the middle and late behavioural phenotypes of Mucopolysaccharidosis Type-III
 | MPS III median ( N, range) | ID median ( N, range) | p value |
---|---|---|---|
ECBI | Â | Â | Â |
 Intensity score | 76 (8, 36–174) | 155 (7, 74–201) | 0.028 |
 Problem score | 1 (7, 0–21) | 14.5 (6, 1–29) | 0.037 |
ABC | Â | Â | Â |
 Irritability | 2 (9, 0–24) | 23 (7, 1–40) | 0.043 |
 Lethargy | 7 (9, 2–28) | 7 (7, 4–27) | 0.915 |
 Stereotypy | 2 (9, 0–14) | 5 (7, 8) | 0.183 |
 Hyperactivity | 7 (9, 2–28) | 23 (7, 1–41) | 0.152 |
 Inappropriate speech | 0 (9,0- 5) | 4 (7, 0–12) | 0.054 |
 ABC total score | 26 (9, 6–80) | 54 (7, 11–106) | 0.081 |
SBRS | Â | Â | Â |
 Current understanding | 10 (10, 2–38) | 33 (7, 14–41) | 0.019 |
 Past understanding | 28 (9, 16–42) | 42 (2, 4–20) | 0.056 |
 Current expression | 2 (10, 0–12) | 11 (7, 5–23) | 0.004 |
 Past expression | 12 (9, 6–24) | 12 (2, 4–20) | 0.813 |
 Orality | 20 (10, 2–36) | 15 (7, 0–26) | 0.243 |
 Body movements | 10 (10, 4–30) | 10 (7, 0–23) | 0.590 |
 Interactions with objects | 11 (10, 3–19) | 8 (7, 0–15) | 0.240 |
 Activity and routines | 14 (10, 4–30) | 20 (7, 6–26) | 0.845 |
 Emotional function | 6 (10, 0–13) | 5 (7, 2–14) | 0.883 |
 Safety consciousness | 12 (10, 0–18) | 8 (7, 3–14) | 0.352 |
 Fearfulness | 28 (10, 12–35) | 16 (7, 8–36) | 0.405 |
 Social interaction | 13.5 (10, 2–22) | 17 (7, 8–25) | 0.282 |
 Eye contact | 3 (10, 0–8) | 6 (7, 0–10) | 0.258 |
 Emotional engagement | 7.5 (10, 4–14) | 6 (7, 2–13) | 0.257 |
 Comfort seeking | 10 (10, 8–14) | 11 (7, 0–20) | 0.428 |
 Attention | 12 (10, 6–18) | 11 (7, 3–18) | 0.883 |
 Self-control/compliance | 6 (10, 0–16) | 10 (7, 4–18) | 0.281 |
 Mood, anger and aggression | 5.5 (10, 0–42) | 19 (7, 2–33) | 0.117 |
 Self-gratification | 0 (10, 0–2) | 2 (7, 0–5) | 0.217 |