From: A national survey of Rett syndrome: behavioural characteristics
Behavioural characteristic | Percentage of sample with characteristic | |||||
---|---|---|---|---|---|---|
Coleman et al. [ 8 ] | Samson et al. [ 9 ] | Mount et al. [ 6 ] | Cass et al. [ 10 ] | Halbach et al. [ 11 ] | This sample | |
( N = 63) | ( N = 107) | ( N = 38) | ( N = 87) | ( N = 53) | ( N = 91) | |
Hand stereotypies | 100 | - | 100 | 97 | - | 99 |
Teeth grinding | 95 | - | 37 | - | - | 58 |
Screaming | 84 | 48 (night) | - | - | 39 (night) | 44 |
Night unrest/laughing | 83 | 84 | 21 | - | 77 | 64 |
Anxiety/inappropriate fear | 75 | 75 | - | - | 68 | 73 |
Low mood/mood changes | - | 70 | - | - | 66 | 77 |
Hyperventilation | 63 | 32 | 84 | 60 | 39 | 63 |
Breath hold | 57 | - | 37 | 41 | 73 | 77 |
Self-injury | 49 | 48 | - | 73 | - | 28 |