Pathology | Location | Total neurons [median] | Dysmorphic neurons [median] | Total Tbr1+ cells [median (range)] | Total Satb2+ cells [median (range)] | Total Cux2+ cells [median (range)] | Total RORβ+ cells [median (range) | Total ER81+ cells [median (range)] | Tbr1+ cells per total neurons [%] | Satb2+ cells per total neurons [%] | Cux2+ cells per total neurons [%] | RORβ+ cells per total neurons [%] | ER81+ cells per total neurons [%] |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Tuber | SG | 399.50 (154.00–899.0) | 96.00 (11.00–238.00) | 41.00 (0.00–126.00) | 63.00 (49.00–161.00) | 43.00 (0.00–145.00) | 88.00 (5.00–198) | 161.00 (99.00–706.00) | 8.00 | 19.00 | 13.00 | 23.00 | 48.00 |
IG | 348.00 (180.00–739) | 111.50 (4.00–204.00) | 94.00 (0.00–178.00) | 2.00 (0.00–136.00) | 13.00 (0.00–112.00) | 134.00 (3.00–165.00) | 206 (96.00–565.00) | 30.00 | 1.00 | 4.00 | 27.00 | 49.00 | |
FCD IIb | SG | 476.00 (439.00–799.00) | 217.00 (175.00–275.00) | 44.00 (13.00–103.00) | 181.00 | 88.00 (0.00–173.00) | 156.00 (15.00–200.00) | 373.00 (175.00–799.00) | 9.00 | 23.00 | 20.00 | 25.00 | 85.00 |
IG | 523.00 (374.00–643.00) | 192.00 (113.00–206.00) | 61.00 (58.00–287.00) | 204.00 | 76.00 (44.00–123.00) | 166.00 (98.00–187.00) | 231.00 (182.00–314.00) | 12.00 | 32.00 | 12.00 | 26.00 | 49.00 | |
PLx | SG | 916.00 (682.00–2263.00) | 0.00 | 176.00 (0.00–460.00) | 193.00 (136.00–315.00) | 345.00 (78.00–660.00) | 121.00 (0.00–264.00) | 227.00 (12.00–652.00) | 16.00 | 19.00 | 37.00 | 10.00 | 27.00 |
IG | 1000.00 (535.00–1242.00) | 0.00 | 420.00 (246.00–662.00) | 14.00 (9.00–215.00) | 99.00 (12.00–276.00) | 452.00 (120.00–688.00) | 519.5 (169.00–987.00) | 44.00 | 3.00 | 16.00 | 55.00 | 64.00 | |
Control | SG | 952.00 (299.00–1175.00) | 0.00 | 14.50 (5.00–24.00) | 548.00 (420.00–676.00) | 367.00 | 49.00 (35.00–63.00) | 65.50 (58.0–73.00) | 0.00 | 36.00 | 39.00 | 12.00 | 19.00 |
IG | 971.00 (842.00–1495.00) | 0.00 | 321.50 (300.00–343.00) | 407.50 (362.00–453.00) | 55.00 | 456.5 (412.00–501.00) | 450.00 (407.00–493.00) | 23.00 | 30.00 | 6.00 | 50.00 | 59.00 |