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Table 7 Median and interquartile ranges of behavioural characteristics, Kruskal-Wallis tests and post hoc Mann-Whitney U test analyses for participant groups: PTHS, AS and CdLS

From: Behavioural and psychological characteristics in Pitt-Hopkins syndrome: a comparison with Angelman and Cornelia de Lange syndromes

 

PTHS

AS

CdLS

Kruskal-Wallis tests

Post hoc comparison: Mann-Whitney U test

h

df

p value

Comparison

U

df

Z

p value

Effect size r

CBQ—Severity

N

17

10

19

       

Median

8

7

7

1.84

2

.4

N/A

IQR

3

3.75

3

MIPQ—Mood

N

24

24

24

       

Median

19

22

18

24.89

2

< .001

PTHS < AS

105

1

3.819

< .001

.55 (large)

IQR

3.75

1

4.75

MIPQ—Interest and Pleasure

N

24

24

24

       

Median

17

17.5

15

2.07

2

.356

N/A

IQR

4.75

5.5

4.75

MIPQ—Total

N

24

24

24

       

Median

36

39.5

34

9.87

2

.007

PTHS < AS

185.5

1

2.121

.034

.31 (medium)

IQR

3.75

7

8.75

RBQ—Total

N

22

23

22

       

Median

12

12

16.5

4.34

2

.114

N/A

IQR

6.5

10

24

RBQ—Stereotyped Behaviour

N

24

23

24

       

Median

10.5

8

9.5

2.85

2

.241

N/A

IQR

4.5

8

6

RBQ—Compulsive Behaviour

N

24

23

24

       

Median

0

0

0

4.23

2

.121

N/A

IQR

0

1

9.75

RBQ—Insistence on Sameness

N

24

24

23

       

Median

0

0

0

1.39

2

.499

N/A

IQR

3

1

6

TAQ—Impulsivity

N

24

24

23

       

Median

15.5

18

15

.552

2

.759

N/A

IQR

9.75

13.5

11

TAQ—Overactivity

N

24

24

23

       

Median

18

19.5

19

.618

2

.734

N/A

IQR

8.75

14

13

TAQ—Total

N

24

24

23

       

Median

33.75

35

32.5

.347

2

.841

N/A

IQR

15.25

22.9

25.8