From: An investigation of the middle and late behavioural phenotypes of Mucopolysaccharidosis Type-III
Domain | Subdomain | MPS III raw score median ( N, range) | MPS III age equivalent (years: months) | ID raw score median ( N, range) | ID age equivalent (years: months) | p value |
---|---|---|---|---|---|---|
Communication | Receptive | 11 (9, 5–16) | 1:0 | 12.5 (10, 6–23) | 1:1 | 0.512 |
Expressive | 17 (9, 9–42) | 0:10 | 13 (10, 8–22) | 0:8 | 0.164 | |
Written | 0 (8, 0–3) | ≤1:10 | 0 (9, 0–14) | ≤1:10 | 0.301 | |
Daily living skills | Personal | 15 (9, 7–26) | 1:5 | 12 (10, 4–34) | 1:2 | 0.870 |
Domestic | 1 (9, 0–10) | 0:10 | 0 (10, 0–8) | ≤0:7 | 0.435 | |
Community | 3 (9, 0–7) | 0:11 | 3 (10, 0–8) | 0:11 | 0.901 | |
Socialisation | Interpersonal relationships | 23 (8, 15–36) | 0:9 | 22.5 (10, 14–43) | 0:8 | 0.447 |
Play and leisure | 13.5 (8, 0–26) | 1:2 | 6 (9, 3–22) | 0:7 | 0.311 | |
Coping skills | 5 (9, 0–18) | 1:1 | 5.5 (0, 0–13) | 1:1 | 0.967 | |
Motor skills | Gross | 59 (7, 46–62) | 2:5 | 42 (10, 12–58) | 1:4 | 0.013 |
 | Fine | 30 (7, 14–37) | 2:8 | 23 (9, 9–28) | 2:0 | 0.050 |