Table 4 VABS Subdomain scores (10–15 year olds)
From: An investigation of the middle and late behavioural phenotypes of Mucopolysaccharidosis Type-III
Domain | Subdomain | Median MPS III score median ( N, range) | MPS III age equivalent (years: months) | Median ID score median ( N, range) | ID age equivalent (years: months) | p value |
|---|---|---|---|---|---|---|
Communication | Receptive | 10.5 (8, 3–33) | 0:11 | 21 (7, 8–28) | 1:9 | 0.223 |
Expressive | 16 (8, 2–90) | 0:9 | 61 (7, 9–73) | 2:10 | 0.165 | |
Written | 0 (8, 0–21) | ≤1:10 | 10 (7, 0–41) | 4:6 | 0.041 | |
Daily living skills | Personal | 11 (8, 0–58) | 1:1 | 40 (7, 14–52) | 2:11 | 0.032 |
Domestic | 0 (8, 0–8) | ≤0:7 | 13 (7, 1–22) | 4:11 | 0.002 | |
Community | 1 (8, 0–24) | 0:3 | 22 (7, 3–23) | 4:10 | 0.022 | |
Socialisation | Interpersonal relationships | 23 (8, 11–47) | 0:9 | 23 (7, 8–42) | 0:9 | 0.449 |
Play and leisure | 12 (8, 2–32) | 1:1 | 14 (6, 8–36) | 1:3 | 0.172 | |
Coping skills | 3.5 (8, 0–29) | 0:7 | 10 (7, 6–17) | 2:1 | 0.031 | |
Motor skills | Gross | 12 (7, 3–79) | 0:7 | 47 (7, 4–67) | 1:8 | 0.096 |
|  | Fine | 16.5 (8, 1–54) | 1:3 | 34 (7, 12–64) | 3:0 | 0.093 |