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Table 6 Median and interquartile range for PTHS and comparison syndrome groups: AS and CdLS, derived from [31] and one-sample Wilcoxon test

From: Behavioural and psychological characteristics in Pitt-Hopkins syndrome: a comparison with Angelman and Cornelia de Lange syndromes

Median scores

PTHS (n = 24)

AS (n = 66) [31]

CdLS (n = 98) [31]

One-sample Wilcoxon test

Comparison group [31]

Z

p value

PTHS significance

Effect size r

SQID familiar—total

Median (IQR)

42.5 (15.25)

53 (48–55)

41.5 (35–48)

AS

3.95

< .001

PTHS < AS

.57 (large)

CdLS

 

.360

  

SQID familiar—receive interaction

Median (IQR)

11.5 (3)

13 (12–14)

10 (8.75–12)

AS

3.21

.001

PTHS < AS

.46 (medium)

CdLS

2.98

.003

PTHS > CdLS

.43 (medium)

SQID familiar—interaction

Median (IQR)

12 (4)

13.5 (12–14)

11 (10–13)

AS

2.90

.004

PTHS < AS

.42 (medium)

CdLS

 

.072

  

SQID familiar—approach or initiate interaction

Median (IQR)

8 (5)

13 (10–14)

10 (7–12)

AS

4.21

< .001

PTHS < AS

.61 (large)

CdLS

2.47

.014

PTHS < CdLS

.36 (medium)

SQID familiar—performance

Median (IQR)

12 (3)

14 (12–14)

11 (9–13)

AS

3.83

< .001

PTHS < AS

.55 (large)

CdLS

 

.528

  

SQID unfamiliar—total

Median (IQR)

35.5 (12.75)

41 (31–48)

26 (13.5–35)

AS

2.88

.004

PTHS < AS

.42 (medium)

CdLS

2.92

.004

PTHS > CdLS

.42 (medium)

SQID unfamiliar—receive interaction

Median (IQR)

9 (3)

10 (8–12)

6.5 (3–8)

AS

 

.108

  

CdLS

3.30

.001

PTHS > CdLS

.48 (medium)

SQID unfamiliar—interaction

Median (IQR)

9.5 (3)

11 (9–12)

7 (3–9)

AS

3.03

.002

PTHS < AS

.44 (medium)

CdLS

2.95

.003

PTHS > CdLS

.43 (medium)

SQID unfamiliar—approach or initiate interaction

Median (IQR)

6 (4.75)

10 (6.75–12)

5 (4–7.5)

AS

3.72

< .001

PTHS < AS

.54 (large)

CdLS

2.33

.020

PTHS > CdLS

.34 (medium)

SQID unfamiliar—performance

Median (IQR)

10 (3)

10 (7–13)

7 (2.75–9)

AS

 

.203

  

CdLS

2.16

.031

PTHS > CdLS

.31 (medium)